Economic and care considerations of Marfan syndrome.

نویسندگان

  • Carl Rudolf Blankart
  • Ricarda Milstein
  • Meike Rybczynski
  • Helke Schüler
  • Yskert von Kodolitsch
چکیده

INTRODUCTION Marfan syndrome is a rare multisystem disease of the connective tissue, which affects multiple organ systems. advances in healthcare have doubled the life-expectancy of patients over the past three decades. to date, there is no comprehensive review that consolidates economic considerations and care for marfan patients. Areas covered: Present research suggests that there may be a link between treatment pattern, disease progression and economic costs of Marfan syndrome. It indicates that an early detection of the disease and preventive interventions achieve a dual aim. From a patient perspective, it may reduce the amount of emergency surgery or intervention, and inpatient stays. In addition, it slows disease progression, lowers lifestyle restrictions, reduces psychological stress, and improves health-related quality of life. Expert commentary: Early detection and preventive measures are likely to achieve a dual aim by simultaneously containing costs and reducing the number and length of inpatient stays.

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عنوان ژورنال:
  • Expert review of pharmacoeconomics & outcomes research

دوره 16 5  شماره 

صفحات  -

تاریخ انتشار 2016